Macrodystrophia lipomatosa: Clinico-patho-radiological correlation
نویسندگان
چکیده
منابع مشابه
Macrodystrophia Lipomatosa: Clinico-patho-radiological Correlation
Macrodystrophia lipomatosa is a rare congenital nonhereditary developmental anomaly. It is characterized by hamartomatous proliferation of the soft tissue leading to disproportionate enlargement of the limbs and digits. Since it leads to diagnostic dilemma, it has to be differentiated from various other conditions as they differ in course, prognosis, complications, and treatment. Herein, we pre...
متن کاملMacrodystrophia Lipomatosa
remaining three ulnar digits appeared normal. Magnetic resonance imaging (MRI) revealed characteristics of macrodystrophia lipomatosa such as enlargement and marked proliferation of the adipose tissues of the left hand, especially the radial aspect. MRI also demonstrated excessive fibrofatty tissue around the affected digits. This tissue has the same signal characteristics as fat on MRI, that i...
متن کاملMacrodystrophia lipomatosa: four case reports
AIM Macrodystrophia lipomatosa is a rare cause of gigantism of limb which can be confused with other common causes like congenital lymphedema. It presents usually with loss of function and cosmetic problems. Four cases are described with emphasis on clinical presentation, differential diagnoses, imaging and treatment options. METHODS & RESULTS Four patients of macrodystrophia lipomatosa were ...
متن کاملMR imaging of macrodystrophia lipomatosa.
Macrodystrophia lipomatosa is a rare nonhereditary congenital form of localised gigantism usually involving the 2nd or 3rd digit of the hand or foot. Pathologically an increase in adipose tissue involving subcutaneous tissue periosteum and bone marrow is present. Typical clinical andradiological appearances are described in this case report. Case Report A 36-year-old female presented with enlar...
متن کاملMacrodystrophia Lipomatosa: A rare presentation
Macrodystrophia lipomatosa is a rare congenital nonhereditary mesenchymal hamartomatous malformation resulting in localized gigantism of parts of extremities that manifests clinically as macrodactyly or megalodactyly. Radiological and Pathological hallmark is the disproportionate fibroadipose tissue proliferation in subcutaneous tissue, nerve sheaths, and periosteum that leads to soft tissue an...
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ژورنال
عنوان ژورنال: Indian Journal of Medical and Paediatric Oncology
سال: 2017
ISSN: 0971-5851
DOI: 10.4103/ijmpo.ijmpo_65_16